BCS1

BT-AP00752

Rabbit

IgG

100ul,50ul,20ul

Polyclonal

Synthesized peptide derived from human BCS1

The antibody was affinity-purified from rabbit serum by affinity-chromatography using specific immunogen.

1 mg/ml

Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.

-20°C for 1 year

This gene encodes a homolog of the S. cerevisiae bcs1 protein which is involved in the assembly of complex III of the mitochondrial respiratory chain. The encoded protein does not contain a mitochondrial targeting sequence but experimental studies confirm that it is imported into mitochondria. Mutations in this gene are associated with mitochondrial complex III deficiency and the GRACILE syndrome. Several alternatively spliced transcripts encoding two different isoforms have been described.

Human: Q9Y276; Mouse: Q9CZP5;

46090

Human: 617; Mouse: 66821

BCS1

Metabolism; Neuroscience; Signal transduction

BCS1L