ECHA

BT-AP09422

Rabbit

IgG

20ul,50ul,100ul

Polyclonal

Synthesized peptide derived from human ECHA

The antibody was affinity-purified from rabbit serum by affinity-chromatography using specific immunogen.

1 mg/ml

Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.301% sodium azide.

-20°C for 1 year

This gene encodes the alpha subunit of the mitochondrial trifunctional protein| which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits| with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation.

Human: P40939; Mouse: Q8BMS1; Rat: Q64428;

Human: 3030; Mouse: 97212; Rat: 170670

ECHA; Trifunctional enzyme subunit alpha; mitochondrial; 78 kDa gastrin-binding protein; TP-alpha) [Includes: Long-chain enoyl-CoA hydratase; EC 4.2.1.17; Long chain 3-hydroxyacyl-CoA dehydrogenase; EC 1.1.1.211;

Cancer; Cardiovascular; Metabolism; Signal transduction; Tags & cell markers

HADHA